Plummer-Vinson Syndrome in Children.

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Plummer-Vinson Syndrome in Children.

J Pediatr Gastroenterol Nutr. 2015 Nov;61(5):547-52

Authors: Butori M, Mahmoudi S, Dugelay-Ecochard E, Belarbi N, Bellaïche M, Hugot JP, Viala J

Abstract
OBJECTIVES: Plummer-Vinson syndrome (PVS), also called Kelly-Paterson syndrome, is a rare cause of dysphagia in children. This syndrome associates single or multiple webs in the upper esophagus with frequent iron deficiency.
METHODS: We reported 3 pediatric cases of PVS before analyzing all of the cases of PVS in children reported in the PubMed and EMBASE databases.
RESULTS: Among 17 reported PVS cases in children, all of the patients experienced iron-deficiency anemia, and no immunological disease was reported. The male/female ratio was 1/1.9, and most cases were observed in adolescents. Conversely to adults, endoscopic dilation was often necessary because dysphagia resisted iron supplementation. A single dilation was usually sufficient. One case of pediatric PVS experienced esophageal cancer in adulthood.
CONCLUSIONS: In the case of dysphagia in children, a swallow barium exploration with lateral incidence should look for PVS. Conversely to adults, an endoscopic dilation is frequently necessary to control dysphagia in children.

PMID: 26502163 [PubMed - indexed for MEDLINE]

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